Phenotype Details
Phene ID
315
Name
Brachyspina
Phene Name
Haplotype HH0
OMIA ID
151
Species ID
9913
Characterised
Yes
Characterised Year
2012
Linked Variants
Variant IDPhenotypeGene IDDeleteriousChromosomeGenomicTranscriptProtein
646Brachyspina170253970121g.20773899_20777226delN/Ap.(V877Lfs*27)
Linked Breeds
BreedBreed IDSpecies IDVBO Term
Holstein (black and white) (Cattle)399913http://purl.obolibrary.org/obo/VBO_0000237
Molecular Genetics

Using mate-pair libraries from one affected and three controls, Charlier et al. (2012) obtained around 3.4Gb of sequence from each animal. Comparison of sequence in the candidate BTA21 region "revealed a 3.3 Kb deletion removing exons 25–27 of the 37 composing the FANCI (Fanconi anemia complementation-group I) gene". Noting that the carrier frequency is far too high (up to 7.4%) to be consistent with a relatively rare autosomal recessive disorder, Charlier et al. (2012) also showed that a large proportion of affected calves die in utero. Thus this causal mutation also contributes to natural abortions and hence to reduced fertility.

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