Phenotype Details
Phene ID
3544
Name
Xanthinuria, type II
Phene Name
N/A
OMIA ID
1819
Species ID
9913
Characterised
Yes
Characterised Year
2000
Linked Variants
Variant IDPhenotypeGene IDDeleteriousChromosomeGenomicTranscriptProtein
446Xanthinuria, type II388161121124NC_037351.1:g.20936257_20936259delNM_174081.2:c.769_771delNP_776506.1:p.(Y257del)
492Xanthinuria, type II388161121124NC_037351.1:g.20911933delXM_024984177.1:c.1881delXP_024839945.1:p.(S628Vfs9*)
Linked Breeds
BreedBreed IDSpecies IDVBO Term
Brown Swiss (Cattle)599913http://purl.obolibrary.org/obo/VBO_0000166
Japanese Black, Japan (Cattle)319913http://purl.obolibrary.org/obo/VBO_0004987
Original Swiss Brown (Cattle)15009913http://purl.obolibrary.org/obo/VBO_0000328
Tiroler Grauvieh (Cattle)13499913http://purl.obolibrary.org/obo/VBO_0000408
Inheritance

Pedigree analysis by Watanabe et al. (2000) revealed autosomal recessive inheritance in Japanese Black cattle. Similar evidence was reported for Tyrolean Grey cattle by Murgiano et al. (2016).

Molecular Genetics

Cloning and sequencing of the bovine gene encoding molybdopterin cofactor sulfurase (MCSU, now called MOCOS) in normal and affected cattle, by Watanabe et al. (2000), revealed the causal mutation to be a 3bp deletion (c.769_771delTAC) of codon 257 (deleting Tyr) in the MOCOS gene (omia.variant:446). Murgiano et al. (2016) discovered a different mutation in the MUCOS gene as the likely cause in Tyrolean Grey cattle: "1 bp deletion in the molybdenum cofactor sulfurase (MOCOS) gene (g.21222030delC; c.1881delG and c.1782delG) [omia.variant:492], located in an 11 Mb region of homozygosity on BTA 24)". Jacinto et al. (2023) reported an affected Brown Swiss animal homozygous for the variant described by Murgiano et al. (2016) (omia.variant:492).

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