Phenotype Details
Phene ID
3894
Name
Retinitis pigmentosa 1
Phene Name
N/A
OMIA ID
2029
Species ID
9913
Characterised
Yes
Characterised Year
2016
Linked Variants
Variant IDPhenotypeGene IDDeleteriousChromosomeGenomicTranscriptProtein
611Retinitis pigmentosa 1388160908114g.22340665_22340666insAN/Ap.(R791Kfs*13)
Linked Breeds
BreedBreed IDSpecies IDVBO Term
Angus (Cattle)449913http://purl.obolibrary.org/obo/VBO_0000104
Belgian Blue (Cattle)499913http://purl.obolibrary.org/obo/VBO_0000139
Charolais (Cattle)199913http://purl.obolibrary.org/obo/VBO_0000177
Gelbvieh (Cattle)619913http://purl.obolibrary.org/obo/VBO_0000212
Holstein Friesian (Cattle)739913http://purl.obolibrary.org/obo/VBO_0000239
Maine-Anjou (Cattle)969913http://purl.obolibrary.org/obo/VBO_0000286
Normande (Cattle)3679913http://purl.obolibrary.org/obo/VBO_0000322
Red Angus (Cattle)1769913http://purl.obolibrary.org/obo/VBO_0000350
Swiss Fleckvieh (Cattle)15029913http://purl.obolibrary.org/obo/VBO_0000393
Molecular Genetics

Michot et al. (2016): "a one base pair insertion (Chr14: g.23995411_23995412insA) that affects the retinitis pigmentosa-1 gene (RP1) . . . [and] is predicted to cause a frameshift at codon 791 and to terminate the protein 13 amino acids later (p. R791KfsX13)".

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