<?xml version="1.0" encoding="UTF-8"?>
<protein>
  <version>1.0</version>
  <creation_date>2018-05-07 22:29:14 UTC</creation_date>
  <update_date>2020-05-20 21:01:47 UTC</update_date>
  <accession>BMDBP01928</accession>
  <secondary_accessions>
  </secondary_accessions>
  <protein_type>Enzyme</protein_type>
  <synonyms>
  </synonyms>
  <gene_name>SCO2</gene_name>
  <general_function>Involved in copper ion binding</general_function>
  <specific_function>Copper metallochaperone essential for the synthesis and maturation of cytochrome c oxidase subunit II (MT-CO2/COX2). Involved in transporting copper to the Cu(A) site on MT-CO2/COX2. Also acts as a thiol-disulfide oxidoreductase to regulate the redox state of the cysteines in SCO1 during maturation of MT-CO2/COX2.</specific_function>
  <pathways>
  </pathways>
  <metabolite_associations>
    <metabolite>
      <accession>BMDB0000657</accession>
      <name>Copper</name>
    </metabolite>
  </metabolite_associations>
  <go_classifications>
  </go_classifications>
  <subcellular_locations>
  </subcellular_locations>
  <gene_properties>
    <chromosome_location>5</chromosome_location>
    <locus/>
    <gene_sequence>&gt;801 bp
ATGCTGCTGCTGGCTCGGCCACCCAAAGCTTGGCACAGGCTCTTTCAGCTCCAGCCTCTG
GCCCTCCTTGGGACCCCAGGAGGCAAGACCCAGCATGTGAGATACCAGCTCTTCTCAACG
CCAGGCCCTGCAGATACAGGCAGGCAGGGCCAGCCCCAGGGTCCCGGCCTGCGAACCAGG
TTGCTCGTCACAGCCCTGGTTGGAGCGGGACTGGGTGGGGCGTGGCTGGCCTTGAGGGCT
GAAAAGGAGCGGGGGCGGCAGCAGCAGCGGACAGAGGCCCTGCGGCAGGCTGCTGTGGGC
CAGGGCGATTTCAGCCTGCTGGACCACCGGGGCCGAGTACGCTGCAAAGCTGACTTCCGG
GGCCAGTGGGTGCTGCTGTACTTCGGCTTCACTCACTGCCCTGACATCTGCCCCGACGAG
CTGGAGAAGTTGGTGCAGGTGGTGCGGCAGCTGGAGGCGGAGCCCGGCCTGCCCCCGGTG
CAGCCCCTCTTCATCACCGTGGACCCCGAGCGGGACACCGTGGCCGCCATGGCCCGCTAC
GTGCAGGACTTCCACCCGAGGCTGCTGGGCCTGACCGGCTCCGCCGAGCAGATCGCCCAG
GTGAGCCGTAGCTACCGCGTGTACTACAGCGCCGGCCCCAAGGACGAAGACCAGGACTAC
ATCGTGGACCACTCCATCGCCATCTACCTGCTCAGCCCTGACGGCCTCTTCACGGACTAC
TACAGCAGGGCCAGGTCAGCCGAGCAGATCACAGACAGCGTGCGGCGCCACATGGCTGCG
TTCCGCAGCGTCCTGCGCTGA</gene_sequence>
  </gene_properties>
  <protein_properties>
    <residue_number>266</residue_number>
    <molecular_weight>29789.0</molecular_weight>
    <theoretical_pi>9.51</theoretical_pi>
    <pfams>
    </pfams>
    <transmembrane_regions>
      <region>61-78</region>
    </transmembrane_regions>
    <signal_regions>
      <region>None</region>
    </signal_regions>
    <polypeptide_sequence>&gt;Protein SCO2 homolog, mitochondrial
MLLLARPPKAWHRLFQLQPLALLGTPGGKTQHVRYQLFSTPGPADTGRQGQPQGPGLRTR
LLVTALVGAGLGGAWLALRAEKERGRQQQRTEALRQAAVGQGDFSLLDHRGRVRCKADFR
GQWVLLYFGFTHCPDICPDELEKLVQVVRQLEAEPGLPPVQPLFITVDPERDTVAAMARY
VQDFHPRLLGLTGSAEQIAQVSRSYRVYYSAGPKDEDQDYIVDHSIAIYLLSPDGLFTDY
YSRARSAEQITDSVRRHMAAFRSVLR</polypeptide_sequence>
  </protein_properties>
  <genbank_protein_id>AAI46151.1</genbank_protein_id>
  <uniprot_id>A6H784</uniprot_id>
  <uniprot_name>SCO2_BOVIN</uniprot_name>
  <pdb_ids>
  </pdb_ids>
  <genbank_gene_id>BC146150</genbank_gene_id>
  <genecard_id>SCO2</genecard_id>
  <geneatlas_id/>
  <general_references>
  </general_references>
  <metabolite_references>
  </metabolite_references>
</protein>
